Developmental changes in craniofacial morphology in subjects with Duchenne muscular dystrophy
نویسندگان
چکیده
منابع مشابه
Developmental changes in craniofacial morphology in subjects with Duchenne muscular dystrophy.
Lateral cephalometric radiographs of 35 Japanese male patients suffering from Duchenne muscular dystrophy (DMD) were taken longitudinally from 10 to 20 years of age. Eighteen landmarks were placed and 15 angles and four linear distances calculated. Profile diagrams (profilograms) were produced to analyse changes in craniofacial morphological growth in the DMD subjects. The measurements were the...
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Duchenne muscular dystrophy (BMD) is an inherited X-link disease. The incidence of this muscle-wasting disease is 1:5000 male live births. Mutation in the gene coding for dystrophin is the main cause of BMD. Most cases of this disease succumb to respiratory and cardiac failure in 3rd to 4th decades. The slow progression of BMD and recent achievement of gene therapies make it as an appropriate c...
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To the Editor With interest we read the article by Misumi et al. about a teenage boy with Duchenne muscular dystrophy (DMD) who had developed dilated cardiomyopathy, isolated left-ventricular hypertrabeculation / noncompaction (LVHT), systolic dysfunction, and fatal ventricular tachycardias (1). We have the following comments and concerns. In Fig. 2, the authors attempt to present LVHT on echoc...
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ژورنال
عنوان ژورنال: European Journal of Orthodontics
سال: 2005
ISSN: 1460-2210,0141-5387
DOI: 10.1093/ejo/cji074